Abnormalities of Teeth qxd

Slide 52:  dentinogenesis imperfecta

Slide 53:  DI type III

---

"Abnormalities of Teeth"

– 8 –

Charles Dunlap, DDS

Sept. 2004

Dentin Dysplasia type I & type II   (DD I & DD II)

Dentin dysplasia type I is a rare dominantly inherited dental developmental abnormality that maps to the same site on

chromosome #4 as does dentinogenesis imperfecta type II & type III. It too may be an allelic variant. The phenotype

varies considerably from solid teeth with no roots and periapical radiolucent lesions

(Slide #54) to teeth with nearly normal root length but with partial obliteration of

the pulp and large pulp stones (Slide #55). The periapical abscesses are due to

extension of the pulp horns nearly to the surface. Minimal occlusal wear exposes

the pulp to oral bacteria. 

Dentin dysplasia type II (coronal DD) is characterized by teeth of nearly normal

length but as the pulp ascends to the crown, it flares into a flame shape or thistle tube

shape as seen in Slides #56 and #57. ( See: "Dentin Dysplasia type I, five cases in

one family." 

Oral Surg Oral Med. Oral Path.

86:175-178  1998)